Robert L. Lebowitz, M.D.
Children' s Hospital, Harvard Medical School
Boston, Massachusetts


Congenital Renal Lymphangiectasia


This 2 1/2-year-old boy presented with intractable ascites.   A CT scan showed the ascites and tiny, cystic lesions around the right kidney that turned out to be dilated lymphatics.(Figure 1). (Figure 2).   No prior treatments had worked to keep his ascites from forming, and he was chronically ill.   He underwent right nephrectomy and the ascites disappeared and he began to thrive.

References:
Simonton SC, et al.   Cystic renal lymphangiectasia: a distinctive clinicopathologic entity in the pediatric age group. &npsb; Pediatr Pathol Lab Med 1997; 17:293-301

Murray KK, McLellan GL.   Renal peripelvic lymphangiectasia: appearance on CT.   Radiology 1991; 180:455-456
 
 

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