Robert L. Lebowitz, M.D. Children' s Hospital, Harvard Medical School Boston, Massachusetts

15-year-old girl presented with primary amenorrhea.  Evaluation showed a solitary hypertrophied right kidney (Figure 1) and no left kidney (Figure 2).  She was found to have vaginal and uterine agenesis(Figure 3).  There is strong correlation between the presence of urinary tract and genital tract anomalies, and the most common renal anomaly is unilateral renal agenesis.